RARE CASE OF CERDJA-STRAUSS SYNDROME
Keywords:
Cherdja-Stross syndrome, diagnosis, lesions of organs and systems, hemogram, myelogram, treatment with hormonesAbstract
Purpose: to identify and diagnose Cherdja-Stross syndrome, which is rare in adult patients.
Materials and methods. Although this condition is a very rare disease - a 64-year-old patient was diagnosed with Cherdja-Stross allergic granulomatous angiitis, in most cases this vasculitis occurs in patients under 35 years of age. The hematological manifestation of the disease was high blood eosinophilia, which was established at the first stage of diagnosis on the basis of sternal puncture and parasitological examination.
Conclusions: Clinically, despite the appearance of primarily severe neurological symptoms, the doctor was able to make a timely diagnosis, as he performed the necessary tests to diagnose systemic vasculitis.
Conclusion. Treatment of the patient showed a positive trend. Recommended: prednisolone 60 mg for 2 weeks according to the scheme, then reduced to a maintenance dose of 5 mg per week - 0.2 mg / kg of body weight per day (with positive dynamics - during the year), symptomatic therapy; cytostatic therapy: cyclophosphamide 200 mg p/o once every 2 days for 2 weeks, then 200 mg p/o 2 times a week for 3 months (or 2 mg/kg per day up to 14 days), then controlled dose reduction of leukocytes in the blood - 1 time per week for 1 month, and then (after stabilization of the number of leukocytes) 1 time in 2 weeks; immunofan 0.005% - 1.0 m / r kun aro No. 5. Confirms the intake of multivitamins in combination with trace elements.
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