FEATURES OF CARRYING OUT CHILDREN WITH PRIMARY CONGENITAL GLAUCOMA ASSOCIATED WITH STERGE-WEBER SYNDROME
Keywords:
Sturge–Weber syndrome, port-wine stain, etamsylate, Maklakov tonometry, iCare 100 tonometryAbstract
The article presents a retrospective and prospective analysis of the examination and treatment outcomes of 21 children with primary congenital glaucoma associated with Sturge–Weber syndrome. Clinical and instrumental features of the disease course are analyzed, including vascular abnormalities of the anterior chamber angle and episcleral vessels and their impact on intraocular pressure. The effectiveness of a combined surgical approach aimed at simultaneous influence on the main aqueous humor outflow pathways, along with preoperative hemostatic preparation, is evaluated. The results demonstrate that the proposed surgical technique provides effective intraocular pressure control in most patients; however, it is associated with a high risk of prolonged postoperative hypotony and choroidal complications. The study concludes that management of glaucoma in children with Sturge –Weber syndrome requires an individualized surgical strategy and careful postoperative monitoring.
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