UTERINE MYOMA IN WOMEN WITH MAYER-ROKITANSKI-KUSTER-HAUSER SYNDROME (Case report)
Keywords:
Mayer Rokitansky-Kuster-Hauser syndrome, uterine myoma, rudimentary uterus, laparoscopy, clinical caseAbstract
Mayer-Rokitansky-Küster-Hauser Syndrome is a congenital disorder involving reproductive, genitourinary, bone, and cardiac malformations. The incidence is 1 in 4000-5000 female live births. The phenotype is female, karyotype 46 XX, with normally developed secondary sexual characteristics and functional ovaries. The occurrence of fibroids from uterine remnants in SMRKH is very rare, although a few cases have been reported in the literature. Diagnosis and approach to treatment in this case is quite complicated. Here we present a clinical case of a 30-year-old woman with SMRKH who was found to have rudimentary uterine fibroids.
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